2006 ICD-9-CM OFFICIAL CODES
DISEASES TABULAR LIST 6
ICDMENU
6. DISEASES OF THE NERVOUS SYSTEM AND SENSE ORGANS (320-389)
INFLAMMATORY DISEASES OF THE CENTRAL NERVOUS SYSTEM (320-326)
320 Bacterial meningitis
Includes: arachnoiditis
bacterial
leptomeningitis bacterial
meningitis bacterial
meningoencephalitis bacterial
meningomyelitis bacterial
pachymeningitis bacterial
320.0 Hemophilus meningitis
Meningitis due to Hemophilus
influenzae [H. influenzae]
320.1 Pneumococcal meningitis
320.2 Streptococcal meningitis
320.3 Staphylococcal meningitis
320.7 Meningitis in other bacterial
diseases classified elsewhere
actinomycosis (039.8)
listeriosis (027.0)
typhoid fever (002.0)
whooping cough (033.0-033.9)
Excludes: meningitis (in):
epidemic (036.0)
gonococcal (098.82)
meningococcal (036.0)
salmonellosis (003.21)
syphilis:
NOS (094.2)
congenital (090.42)
meningovascular (094.2)
secondary (091.81)
tuberculosis (013.0)
320.8 Meningitis due to other specified
bacteria
320.81
Anaerobic meningitis
Gram-negative anaerobes
Bacteroides (fragilis)
320.82
Meningitis due to gram-negative bacteria, not elsewhere
classified
Aerobacter aerogenes
Escherichia coli [E. coli]
Friedlander bacillus
Klebsiella pneumoniae
Proteus morganii
Pseudomonas
Excludes: gram-negative anaerobes (320.81)
320.89
Meningitis due to other specified bacteria
Bacillus pyocyaneus
320.9 Meningitis due to unspecified
bacterium
Meningitis:
bacterial NOS
purulent NOS
pyogenic NOS
suppurative NOS
321 Meningitis due to other organisms
Includes: arachnoiditis due
to organisms other than bacteria
leptomeningitis due to organisms other than bacteria
meningitis due to organisms other than bacteria
pachymeningitis due to organisms other than bacteria
321.0 Cryptococcal meningitis
321.1 Meningitis in other fungal
diseases
Excludes: meningitis in:
candidiasis (112.83)
coccidioidomycosis (114.2)
histoplasmosis (115.01, 115.11, 115.91)
321.2 Meningitis due to viruses not
elsewhere classified
meningitis due to arbovirus (060.0-066.9)
Excludes: meningitis (due to):
abacterial (047.0-047.9)
adenovirus (049.1)
aseptic NOS (047.9)
Coxsackie (virus) (047.0)
ECHO virus (047.1)
enterovirus (047.0-047.9)
herpes simplex virus (054.72)
herpes zoster virus (053.0)
lymphocytic choriomeningitis virus (049.0)
mumps (072.1)
viral NOS (047.9)
meningo-eruptive syndrome (047.1)
321.3 Meningitis due to trypanosomiasis
321.4 Meningitis in sarcoidosis
321.8 Meningitis due to other
nonbacterial organisms classified elsewhere
Excludes: leptospiral meningitis (100.81)
322 Meningitis of unspecified cause
Includes: arachnoiditis with
no organism specified as cause
leptomeningitis with no organism specified as cause
meningitis with no organism specified as cause
pachymeningitis with no organism specified as cause
322.0 Nonpyogenic meningitis
Meningitis with clear
cerebrospinal fluid
322.1 Eosinophilic meningitis
322.2 Chronic meningitis
322.9 Meningitis, unspecified
323 Encephalitis, myelitis, and encephalomyelitis
Includes: acute disseminated
encephalomyelitis
meningoencephalitis, except bacterial
meningomyelitis, except bacterial
myelitis (acute):
ascending
transverse
Excludes: bacterial:
meningoencephalitis (320.0-320.9)
meningomyelitis (320.0-320.9)
323.0 Encephalitis in viral diseases
classified elsewhere
cat-scratch disease (078.3)
infectious mononucleosis (075)
ornithosis (073.7)
Excludes: encephalitis (in):
arthropod-borne viral (062.0-064)
herpes simplex (054.3)
mumps (072.2)
poliomyelitis (045.0-045.9)
rubella (056.01)
slow virus infections of central nervous system (046.0-046.9)
other viral diseases of central nervous system (049.8-049.9)
viral NOS (049.9)
323.1 Encephalitis in rickettsial
diseases classified elsewhere
323.2 Encephalitis in protozoal
diseases classified elsewhere
malaria (084.0-084.9)
trypanosomiasis (086.0-086.9)
323.4 Other encephalitis due to
infection classified elsewhere
Excludes: encephalitis (in):
meningococcal (036.1)
syphilis:
NOS (094.81)
congenital (090.41)
toxoplasmosis (130.0)
tuberculosis (013.6)
meningoencephalitis due to free-living ameba [Naegleria]
(136.2)
323.5 Encephalitis following
immunization procedures
Encephalitis postimmunization
or postvaccinal
Encephalomyelitis
postimmunization or postvaccinal
Use additional E code to
identify vaccine
323.6 Postinfectious encephalitis
Infectious acute disseminated
encephalomyelitis (ADEM)
Excludes: encephalitis:
postchickenpox (052.0)
postmeasles (055.0)
323.7 Toxic encephalitis
carbon tetrachloride (982.1)
hydroxyquinoline derivatives
(961.3)
lead (984.0-984.9)
mercury (985.0)
thallium (985.8)
323.8 Other causes of encephalitis
Noninfectious acute disseminated
encephalomyelitis (ADEM)
323.9 Unspecified cause of encephalitis
324 Intracranial and intraspinal abscess
324.0 Intracranial abscess
Abscess (embolic):
cerebellar
cerebral
Abscess (embolic) of brain [any
part]:
epidural
extradural
otogenic
subdural
Excludes: tuberculous (013.3)
324.1 Intraspinal abscess
Abscess (embolic) of spinal cord
[any part]:
epidural
extradural
subdural
Excludes: tuberculous (013.5)
324.9 Of unspecified site
Extradural or subdural
abscess NOS
325 Phlebitis and thrombophlebitis of intracranial venous
sinuses
Embolism of cavernous, lateral, or other intracranial or
unspecified
intracranial venous sinus
Endophlebitis of cavernous, lateral, or other intracranial
or unspecified
intracranial venous sinus
Phlebitis, septic or suppurative of cavernous, lateral, or
other
intracranial or unspecified intracranial venous sinus
Thrombophlebitis of cavernous, lateral, or other
intracranial or unspecified
intracranial venous sinus
Thrombosis of cavernous, lateral, or other intracranial or
unspecified
intracranial venous sinus
Excludes: that specified as:
complicating pregnancy, childbirth, or the puerperium (671.5)
of nonpyogenic origin (437.6)
326 Late effects of intracranial abscess or pyogenic
infection
Note: This category is to be used to indicate conditions whose
primary
classification is to 320-325 [excluding 320.7, 321.0-321.8,
323.0-323.4,
323.6-323.7] as the cause of late
effects, themselves classifiable
elsewhere. The "late effects" include conditions
specified as such, or as
sequelae, which may occur at any time after the resolution
of the causal
condition.
Use additional code to identify condition, as:
hydrocephalus (331.4)
paralysis (342.0-342.9, 344.0-344.9)
327 Organic sleep disorders
327.0 Organic disorders of initiating
and maintaining sleep [Organic
insomnia]
Excludes: insomnia NOS (780.52)
insomnia not due to a substance or known physiological
condition (307.41-307.42)
insomnia with sleep apnea NOS (780.51)
327.00
Organic insomnia, unspecified
327.01
Insomnia due to medical condition classified elsewhere
Excludes: insomnia due to mental
disorder (327.02)
327.02
Insomnia due to mental disorder
Excludes: alcohol induced insomnia (291.82)
drug induced insomnia (292.85)
327.09
Other organic insomnia
327.1 Organic disorder of excessive
somnolence [Organic hypersomnia]
Excludes: hypersomnia NOS (780.54)
hypersomnia not due to a substance or known physiological
condition (307.43-307.44)
hypersomnia with sleep apnea NOS (780.53)
327.10
Organic hypersomnia, unspecified
327.11
Idiopathic hypersomnia with long sleep time
327.12
Idiopathic hypersomnia without long sleep time
327.13
Recurrent hypersomnia
Kleine-Levin syndrome
Menstrual related hypersomnia
327.14
Hypersomnia due to medical condition classified elsewhere
Excludes: hypersomnia due to mental
disorder (327.15)
327.15
Hypersomnia due to mental disorder
Excludes: alcohol induced insomnia (291.82)
drug induced insomnia (292.85)
327.19
Other organic hypersomnia
327.2 Organic sleep apnea
Excludes: Cheyne-Stokes breathing (786.04)
hypersomnia with sleep apnea NOS (780.53)
insomnia with sleep apnea NOS (780.51)
sleep apnea in newborn (770.81-770.82)
sleep apnea NOS (780.57)
327.20
Organic sleep apnea, unspecified
327.21
Primary central sleep apnea
327.22
High altitude periodic breathing
327.23 Obstructive sleep apnea
(adult) (pediatric)
327.24
Idiopathic sleep related nonobstructive alveolar hypoventilation
Sleep related hypoxia
327.25
Congenital central alveolar hypoventilation syndrome
327.26
Sleep related hypoventilation/hypoxemia in conditions
classifiable elsewhere
327.27
Central sleep apnea in conditions classified elsewhere
327.29
Other organic sleep apnea
327.3 Circadian rhythm sleep disorder
Organic disorder of sleep
wake cycle
Organic disorder of sleep
wake schedule
Excludes: alcohol induced circadian
rhythm sleep disorder (291.82)
circadian rhythm sleep disorder of nonorganic origin (307.45)
disruption of 24 hour sleep wake cycle NOS (780.55)
drug induced circadian rhythm sleep disorder (292.85)
327.30
Circadian rhythm sleep disorder, unspecified
327.31
Circadian rhythm sleep disorder, delayed sleep phase type
327.32
Circadian rhythm sleep disorder, advanced sleep phase type
327.33
Circadian rhythm sleep disorder, irregular sleep-wake type
327.34
Circadian rhythm sleep disorder, free-running type
327.35
Circadian rhythm sleep disorder, jet lag type
327.36
Circadian rhythm sleep disorder, shift work type
327.37
Circadian rhythm sleep disorder in conditions classified
elsewhere
327.39
Other circadian rhythm sleep disorder
327.4 Organic parasomnia
Excludes: alcohol induced
parasomnia (291.82)
drug induced parasomnia (292.85)
parasomnia not due to a known physiological conditions
(307.47)
327.40
Organic parasomnia, unspecified
327.41
Confusional arousals
327.42
REM sleep behavior disorder
327.43
Recurrent isolated sleep paralysis
327.44
Parasomnia in conditions classified elsewhere
327.49
Other organic parasomnia
327.5 Organic sleep related movement
disorders
Excludes: restless leg syndrome (333.99)
sleep related movement disorder NOS (780.58)
327.51
Periodic limb movement disorder
Periodic limb movement sleep disorder
327.52
Sleep related leg cramps
327.53
Sleep related bruxism
327.59
Other organic sleep related movement disorders
327.8 Other organic sleep disorders
HEREDITARY AND DEGENERATIVE DISEASES OF THE CENTRAL NERVOUS SYSTEM (330-337)
Excludes: hepatolenticular
degeneration (275.1)
multiple sclerosis (340)
other demyelinating diseases of central nervous system
(341.0-341.9)
330 Cerebral degenerations usually manifest in childhood
Use additional code to identify associated mental retardation
330.0 Leukodystrophy
Krabbe's disease
Leukodystrophy:
NOS
globoid cell
metachromatic
sudanophilic
Pelizaeus-Merzbacher disease
Sulfatide lipidosis
330.1 Cerebral lipidoses
Amaurotic (familial) idiocy
Disease:
Batten
Jansky-Bielschowsky
Kufs'
Spielmeyer-Vogt
Tay-Sachs
Gangliosidosis
330.2 Cerebral degeneration in
generalized lipidoses
Fabry's disease (272.7)
Gaucher's disease (272.7)
Niemann-Pick disease (272.7)
sphingolipidosis (272.7)
330.3 Cerebral degeneration of
childhood in other diseases classified
elsewhere
Hunter's disease (277.5)
mucopolysaccharidosis (277.5)
330.8 Other specified cerebral
degenerations in childhood
Alpers' disease or
gray-matter degeneration
Infantile necrotizing
encephalomyelopathy
Leigh's disease
Subacute necrotizing
encephalopathy or encephalomyelopathy
330.9 Unspecified cerebral degeneration
in childhood
331 Other cerebral degenerations
331.0 Alzheimer's disease
331.1 Frontotemporal dementia
Use additional code for associated behavioral disturbances (294.10-294.11)
331.11
Pick's disease
331.19
Other frontotemporal dementia
Frontal dementia
331.2 Senile degeneration of brain
Excludes: senility NOS (797)
331.3 Communicating hydrocephalus
Excludes: congenital hydrocephalus (741.0, 742.3)
331.4 Obstructive hydrocephalus
Acquired hydrocephalus NOS
Excludes: congenital hydrocephalus (741.0, 742.3)
331.7 Cerebral degeneration in diseases
classified elsewhere
alcoholism (303.0-303.9)
beriberi (265.0)
cerebrovascular disease (430-438)
congenital hydrocephalus (741.0, 742.3)
neoplastic disease (140.0-239.9)
myxedema (244.0-244.9)
vitamin B12 deficiency (266.2)
Excludes: cerebral
degeneration in:
Jakob-Creutzfeldt disease (046.1)
progressive multifocal leukoencephalopathy (046.3)
subacute spongiform encephalopathy (046.1)
331.8 Other cerebral degeneration
331.81
Reye's syndrome
331.82
Dementia with Lewy bodies
Dementia with Parkinsonism
Lewy body dementia
Lewy body disease
Use additional code for associated behavioral disturbances (294.10-294.11)
331.89
Other
Cerebral ataxia
331.9 Cerebral degeneration,
unspecified
332 Parkinson's disease
Excludes: dementia with
Parkinsonism (331.82)
332.0 Paralysis agitans
Parkinsonism or Parkinson's
disease:
NOS
idiopathic
primary
332.1 Secondary Parkinsonism
Neuroleptic-induced
Parkinsonism
Parkinsonism due to drugs
Use additional E code to
identify drug, if drug-induced
Excludes: Parkinsonism (in):
Huntington's disease (333.4)
progressive supranuclear palsy (333.0)
Shy-Drager syndrome (333.0)
syphilitic (094.82)
333 Other extrapyramidal disease and abnormal movement
disorders
Includes: other forms of
extrapyramidal, basal ganglia, or
striatopallidal disease
Excludes: abnormal movements of
head NOS (781.0)
sleep related movement disorders (327.51-327.59)
333.0 Other degenerative diseases of
the basal ganglia
Atrophy or degeneration:
olivopontocerebellar
[Déjérine-Thomas syndrome]
pigmentary pallidal
[Hallervorden-Spatz disease] striatonigral
Parkinsonian syndrome
associated with:
idiopathic orthostatic
hypotension
symptomatic orthostatic
hypotension
Progressive supranuclear
ophthalmoplegia
Shy-Drager syndrome
333.1 Essential and other specified
forms of tremor
Benign essential tremor
Familial tremor
Medication-induced postural
tremor
Use additional E code to
identify drug, if drug-induced
Excludes: tremor NOS (781.0)
333.2 Myoclonus
Familial essential myoclonus
Progressive myoclonic
epilepsy
Unverricht-Lundborg disease
Use additional E code to
identify drug, if drug-induced
333.3 Tics of organic origin
Excludes: Gilles de la Tourette's
syndrome (307.23)
habit spasm (307.22)
tic NOS (307.20)
Use additional E code to identify drug, if drug-induced
333.4 Huntington's chorea
333.5 Other choreas
Hemiballism(us)
Paroxysmal choreo-athetosis
Excludes: Sydenham's or rheumatic
chorea (392.0-392.9)
Use additional E code to identify drug, if drug-induced
333.6 Idiopathic torsion dystonia
Dystonia:
deformans progressiva
musculorum deformans
(Schwalbe-) Ziehen-Oppenheim
disease
333.7 Symptomatic torsion dystonia
Athetoid cerebral palsy
[Vogt's disease]
Double athetosis (syndrome)
Neuroleptic-induced acute
dystonia
Use additional E code to
identify drug, if drug-induced
333.8 Fragments of torsion dystonia
Use additional E code to
identify drug, if drug-induced
333.81
Blepharospasm
333.82
Orofacial dyskinesia
Neuroleptic-induced tardive dyskinesia
333.83
Spasmodic torticollis
Excludes: torticollis:
NOS (723.5)
hysterical (300.11)
psychogenic (306.0)
333.84
Organic writers' cramp
Excludes: psychogenic (300.89)
333.89
Other
333.9 Other and unspecified
extrapyramidal diseases and abnormal movement
disorders
333.90
Unspecified extrapyramidal disease and abnormal movement disorder
Medication-induced movement disorders NOS
Use additional E code to identify drug, if drug-induced
333.91
Stiff-man syndrome
333.92
Neuroleptic malignant syndrome
Use additional E to identify drug
333.93
Benign shuddering attacks
333.99
Other
Neuroleptic-induced acute akathisia
Restless legs
Use additional E code to identify drug, if drug-induced
334 Spinocerebellar disease
Excludes: olivopontocerebellar
degeneration (333.0)
peroneal muscular atrophy (356.1)
334.0 Friedreich's ataxia
334.1 Hereditary spastic paraplegia
334.2 Primary cerebellar degeneration
Cerebellar ataxia:
Marie's
Sanger-Brown
Dyssynergia cerebellaris
myoclonica
Primary cerebellar
degeneration:
NOS
hereditary
sporadic
334.3 Other cerebellar ataxia
Cerebellar ataxia NOS
Use additional E code to
identify drug, if drug-induced
334.4 Cerebellar ataxia in diseases
classified elsewhere
alcoholism (303.0-303.9)
myxedema (244.0-244.9)
neoplastic disease (140.0-239.9)
334.8 Other spinocerebellar diseases
Ataxia-telangiectasia
[Louis-Bar syndrome]
Corticostriatal-spinal
degeneration
334.9 Spinocerebellar disease,
unspecified
335 Anterior horn cell disease
335.0 Werdnig-Hoffmann disease
Infantile spinal muscular
atrophy
Progressive muscular atrophy
of infancy
335.1 Spinal muscular atrophy
335.10
Spinal muscular atrophy, unspecified
335.11
Kugelberg-Welander disease
Spinal muscular atrophy:
familial
juvenile
335.19
Other
Adult spinal muscular atrophy
335.2 Motor neuron disease
335.20
Amyotrophic lateral sclerosis
Motor neuron disease (bulbar) (mixed type)
335.21
Progressive muscular atrophy
Duchenne-Aran muscular atrophy
Progressive muscular atrophy (pure)
335.22
Progressive bulbar palsy
335.23
Pseudobulbar palsy
335.24
Primary lateral sclerosis
335.29
Other
335.8 Other anterior horn cell diseases
335.9 Anterior horn cell disease,
unspecified
336 Other diseases of spinal cord
336.0 Syringomyelia and syringobulbia
336.1 Vascular myelopathies
Acute infarction of spinal cord
(embolic) (nonembolic)
Arterial thrombosis of spinal
cord
Edema of spinal cord
Hematomyelia
Subacute necrotic myelopathy
336.2 Subacute combined degeneration of
spinal cord in diseases classified
elsewhere
pernicious anemia (281.0)
other vitamin B12 deficiency anemia
(281.1)
vitamin B12 deficiency (266.2)
336.3 Myelopathy in other diseases
classified elsewhere
myelopathy in neoplastic disease (140.0-239.9)
Excludes: myelopathy in:
intervertebral disc disorder (722.70-722.73)
spondylosis (721.1, 721.41-721.42, 721.91)
336.8 Other myelopathy
Myelopathy:
drug-induced
radiation-induced
Use additional E code to
identify cause
336.9 Unspecified disease of spinal
cord
Cord compression NOS
Myelopathy NOS
Excludes: myelitis (323.0-323.9)
spinal (canal) stenosis (723.0, 724.00-724.09)
337 Disorders of the autonomic nervous system
Includes: disorders of
peripheral autonomic, sympathetic,
parasympathetic, or vegetative system
Excludes: familial dysautonomia
[Riley-Day syndrome] (742.8)
337.0 Idiopathic peripheral autonomic
neuropathy
Carotid sinus syncope or
syndrome
Cervical sympathetic
dystrophy or paralysis
337.1 Peripheral autonomic neuropathy
in disorders classified elsewhere
amyloidosis (277.3)
diabetes (250.6)
337.2 Reflex sympathetic dystrophy
337.20
Reflex sympathetic dystrophy, unspecified
337.21
Reflex sympathetic dystrophy of the upper limb
337.22
Reflex sympathetic dystrophy of the lower limb
337.29
Reflex sympathetic dystrophy of other specified site
337.3 Autonomic dysreflexia
Use additional code to identify the cause, such as:
decubitus ulcer (707.00-707.09)
fecal impaction (560.39)
urinary tract infection (599.0)
337.9 Unspecified disorder of autonomic
nervous system
OTHER DISORDERS OF THE CENTRAL NERVOUS SYSTEM (340-349)
340 Multiple sclerosis
Disseminated or multiple sclerosis:
NOS
brain stem
cord
generalized
341 Other demyelinating diseases of central nervous system
341.0 Neuromyelitis optica
341.1 Schilder's disease
Balo's concentric sclerosis
Encephalitis periaxialis:
concentrica [Balo's]
diffusa [Schilder's]
341.8 Other demyelinating diseases of
central nervous system
Central demyelination of
corpus callosum
Central pontine myelinosis
Marchiafava (-Bignami) disease
341.9 Demyelinating disease of central
nervous system, unspecified
342 Hemiplegia and hemiparesis
Note: This category is to be used when hemiplegia (complete)
(incomplete) is
reported without further specification, or is stated to be
old or
long-standing but of unspecified cause. The category is
also for use in
multiple coding to identify these types of hemiplegia
resulting from any
cause.
Excludes: congenital (343.1)
hemiplegia due to late effect of cerebrovascular accident
(438.20-438.22)
infantile NOS (343.4)
The following fifth-digits are for use with codes 342.0-342.9
0 affecting unspecified side
1 affecting dominant side
2 affecting nondominant side
342.0_
Flaccid hemiplegia
342.1_
Spastic hemiplegia
342.8_
Other specified hemiplegia
342.9_
Hemiplegia, unspecified
343 Infantile cerebral palsy
Includes: cerebral:
palsy NOS
spastic infantile paralysis
congenital spastic paralysis (cerebral)
Little's disease
paralysis (spastic) due to birth injury:
intracranial
spinal
Excludes: hereditary cerebral
paralysis, such as:
hereditary spastic paraplegia (334.1)
Vogt's disease (333.7)
spastic paralysis specified as noncongenital or noninfantile
(344.0-344.9)
343.0 Diplegic
Congenital diplegia
Congenital paraplegia
343.1 Hemiplegic
Congenital hemiplegia
Excludes: infantile hemiplegia NOS (343.4)
343.2 Quadriplegic
Tetraplegic
343.3 Monoplegic
343.4 Infantile hemiplegia
Infantile hemiplegia (postnatal)
NOS
343.8 Other specified infantile
cerebral palsy
343.9 Infantile cerebral palsy,
unspecified
Cerebral palsy NOS
344 Other paralytic syndromes
Note: This category is to be used when the listed conditions are
reported
without further specification or are stated to be old or
long-standing but
of unspecified cause. The category is also for use in
multiple coding to
identify these conditions resulting from any cause.
Includes: paralysis (complete)
(incomplete), except as classifiable to
342 and 343
Excludes: congenital or infantile
cerebral palsy (343.0-343.9)
hemiplegia (342.0-342.9)
congenital or infantile (343.1, 343.4)
344.0 Quadriplegia and quadriparesis
344.00
Quadriplegia, unspecified
344.01
C1-C4, complete
344.02
C1-C4, incomplete
344.03
C5-C7, complete
344.04
C5-C7, incomplete
344.09
Other
344.1 Paraplegia
Paralysis of both lower limbs
Paraplegia (lower)
344.2 Diplegia of upper limbs
Diplegia (upper)
Paralysis of both upper limbs
344.3 Monoplegia of lower limb
Paralysis of lower limb
Excludes: monoplegia of lower
limb due to late effect of
cerebrovascular accident (438.40-438.42)
344.30
Affecting unspecified side
344.31
Affecting dominant side
344.32
Affecting nondominant side
344.4 Monoplegia of upper limb
Paralysis of upper limb
Excludes: monoplegia of upper
limb due to late effect of
cerebrovascular accident (438.30-438.32)
344.40
Affecting unspecified side
344.41
Affecting dominant side
344.42
Affecting nondominant side
344.5 Unspecified monoplegia
344.6 Cauda equina syndrome
344.60
Without mention of neurogenic bladder
344.61
With neurogenic bladder
Acontractile bladder
Autonomic hyperreflexia of bladder
Cord bladder
Detrusor hyperreflexia
344.8 Other specified paralytic
syndromes
344.81
Locked-in state
344.89
Other specified paralytic syndrome
344.9 Paralysis, unspecified
345 Epilepsy
The following fifth-digit subclassification is for use with
categories 345.0,
.1, .4-.9:
0 without mention of intractable epilepsy
1 with intractable epilepsy
Excludes: progressive myoclonic
epilepsy (333.2)
345.0_
Generalized nonconvulsive epilepsy
Absences:
atonic
typical
Minor epilepsy
Petit mal
Pykno-epilepsy
Seizures:
akinetic
atonic
345.1_
Generalized convulsive epilepsy
Epileptic seizures:
clonic
myoclonic
tonic
tonic-clonic
Grand mal
Major epilepsy
Excludes: convulsions:
NOS (780.3)
infantile (780.3)
newborn (779.0)
infantile spasms (345.6)
345.2 Petit mal status
Epileptic absence status
345.3 Grand mal status
Status epilepticus NOS
Excludes: epilepsia partialis
continua (345.7) status:
psychomotor (345.7)
temporal lobe (345.7)
345.4_
Partial epilepsy, with impairment of consciousness
Epilepsy:
limbic system
partial:
secondarily generalized
with memory and ideational disturbances
psychomotor
psychosensory
temporal lobe
Epileptic automatism
345.5_
Partial epilepsy, without mention of impairment of consciousness
Epilepsy:
Bravais-Jacksonian NOS
focal (motor) NOS
Jacksonian NOS
motor partial
partial NOS
sensory-induced
somatomotor
somatosensory
visceral
visual
345.6_
Infantile spasms
Hypsarrhythmia
Lightning spasms
Salaam attacks
Excludes: salaam tic (781.0)
345.7_
Epilepsia partialis continua
Kojevnikov's epilepsy
345.8_
Other forms of epilepsy
Epilepsy:
cursive [running]
gelastic
345.9_
Epilepsy, unspecified
Epileptic convulsions, fits, or seizures NOS
Excludes: convulsive seizure or fit
NOS (780.3)
346 Migraine
The following fifth-digit subclassification is for use with
category 346:
0 without mention of intractable migraine
1 with intractable migraine, so stated
346.0_
Classical migraine
Migraine preceded or accompanied by transient focal neurological
phenomena
Migraine with aura
346.1_
Common migraine
Atypical migraine
Sick headache
346.2_
Variants of migraine
Cluster headache
Histamine cephalgia
Horton's neuralgia
Migraine:
abdominal
basilar
lower half
retinal
Neuralgia:
ciliary
migrainous
346.8_
Other forms of migraine
Migraine:
hemiplegic
ophthalmoplegic
346.9_
Migraine, unspecified
347 Cataplexy and narcolepsy
347.0 Narcolepsy
347.00
Without cataplexy
Narcolepsy NOS
347.01
With cataplexy
347.1 Narcolepsy in conditions
classified elsewhere
347.10
Without cataplexy
347.11
With cataplexy
348 Other conditions of brain
348.0 Cerebral cysts
Arachnoid cyst
Porencephalic cyst
Porencephaly, acquired
Pseudoporencephaly
348.1 Anoxic brain damage
Excludes: that occurring in:
abortion (634-638 with .7, 639.8)
ectopic or molar pregnancy (639.8)
labor or delivery (668.2, 669.4)
that of newborn (767.0, 768.0-768.9, 772.1-772.2)
Use additional E code to identify cause
348.2 Benign intracranial hypertension
Pseudotumor cerebri
Excludes: hypertensive
encephalopathy (437.2)
348.3 Encephalopathy, not elsewhere
classified
348.30
Encephalopathy, unspecified
348.31
Metabolic encephalopathy
Septic encephalopathy
348.39
Other encephalopathy
Excludes: encephalopathy:
alcoholic (291.2)
hepatic (572.2)
hypertensive (437.2)
toxic (349.82)
348.4 Compression of brain
Compression brain (stem)
Herniation brain (stem)
Posterior fossa compression
syndrome
348.5 Cerebral edema
348.8 Other conditions of brain
Cerebral:
calcification
fungus
348.9 Unspecified condition of brain
349 Other and unspecified disorders of the nervous system
349.0 Reaction to spinal or lumbar
puncture
Headache following lumbar
puncture
349.1 Nervous system complications from
surgically implanted device
Excludes: immediate postoperative
complications (997.00-997.09)
mechanical complications of nervous system device (996.2)
349.2 Disorders of meninges, not
elsewhere classified
Adhesions, meningeal (cerebral)
(spinal)
Cyst, spinal meninges
Meningocele, acquired
Pseudomeningocele, acquired
349.8 Other specified disorders of
nervous system
349.81
Cerebrospinal fluid rhinorrhea
Excludes: cerebrospinal fluid
otorrhea (388.61)
349.82
Toxic encephalopathy
Use additional E code to identify cause
349.89
Other
349.9 Unspecified disorders of nervous
system
Disorder of nervous system
(central) NOS
DISORDERS OF THE PERIPHERAL NERVOUS SYSTEM (350-359)
Excludes: diseases of:
acoustic [8th] nerve (388.5)
oculomotor [3rd, 4th, 6th] nerves (378.0-378.9)
optic [2nd] nerve (377.0-377.9)
peripheral autonomic nerves (337.0-337.9)
neuralgia NOS or "rheumatic" (729.2)
neuritis NOS or "rheumatic" (729.2)
radiculitis NOS or "rheumatic" (729.2)
peripheral neuritis in pregnancy (646.4)
350 Trigeminal nerve disorders
Includes: disorders of 5th
cranial nerve
350.1 Trigeminal neuralgia
Tic douloureux
Trifacial neuralgia
Trigeminal neuralgia NOS
Excludes: postherpetic (053.12)
350.2 Atypical face pain
350.8 Other specified trigeminal nerve
disorders
350.9 Trigeminal nerve disorder,
unspecified
351 Facial nerve disorders
Includes: disorders of 7th
cranial nerve
Excludes: that in newborn (767.5)
351.0 Bell's palsy
Facial palsy
351.1 Geniculate ganglionitis
Geniculate ganglionitis NOS
Excludes: herpetic (053.11)
351.8 Other facial nerve disorders
Facial myokymia
Melkersson's syndrome
351.9 Facial nerve disorder,
unspecified
352 Disorders of other cranial nerves
352.0 Disorders of olfactory [1st]
nerve
352.1 Glossopharyngeal neuralgia
352.2 Other disorders of
glossopharyngeal [9th] nerve
352.3 Disorders of pneumogastric [10th]
nerve
Disorders of vagal nerve
Excludes: paralysis of vocal cords
or larynx (478.30-478.34)
352.4 Disorders of accessory [11th]
nerve
352.5 Disorders of hypoglossal [12th]
nerve
352.6 Multiple cranial nerve palsies
Collet-Sicard syndrome
Polyneuritis cranialis
352.9 Unspecified disorder of cranial
nerves
353 Nerve root and plexus disorders
Excludes: conditions due to:
intervertebral disc disorders (722.0-722.9)
spondylosis (720.0-721.9)
vertebrogenic disorders (723.0-724.9)
353.0 Brachial plexus lesions
Cervical rib syndrome
Costoclavicular syndrome
Scalenus anticus syndrome
Thoracic outlet syndrome
Excludes: brachial neuritis or
radiculitis NOS (723.4)
that in newborn (767.6)
353.1 Lumbosacral plexus lesions
353.2 Cervical root lesions, not
elsewhere classified
353.3 Thoracic root lesions, not
elsewhere classified
353.4 Lumbosacral root lesions, not
elsewhere classified
353.5 Neuralgic amyotrophy
Parsonage-Aldren-Turner
syndrome
353.6 Phantom limb (syndrome)
353.8 Other nerve root and plexus
disorders
353.9 Unspecified nerve root and plexus
disorder
354 Mononeuritis of upper limb and mononeuritis multiplex
354.0 Carpal tunnel syndrome
Median nerve entrapment
Partial thenar atrophy
354.1 Other lesion of median nerve
Median nerve neuritis
354.2 Lesion of ulnar nerve
Cubital tunnel syndrome
Tardy ulnar nerve palsy
354.3 Lesion of radial nerve
Acute radial nerve palsy
354.4 Causalgia of upper limb
Excludes: causalgia:
NOS (355.9)
lower limb (355.71)
354.5 Mononeuritis multiplex
Combinations of single
conditions classifiable to 354 or 355
354.8 Other mononeuritis of upper limb
354.9 Mononeuritis of upper limb,
unspecified
355 Mononeuritis of lower limb
355.0 Lesion of sciatic nerve
Excludes: sciatica NOS (724.3)
355.1 Meralgia paresthetica
Lateral cutaneous femoral
nerve of thigh compression or syndrome
355.2 Other lesion of femoral nerve
355.3 Lesion of lateral popliteal nerve
Lesion of common peroneal
nerve
355.4 Lesion of medial popliteal nerve
355.5 Tarsal tunnel syndrome
355.6 Lesion of plantar nerve
Morton's metatarsalgia,
neuralgia, or neuroma
355.7 Other mononeuritis of lower limb
355.71
Causalgia of lower limb
Excludes: causalgia:
NOS (355.9)
upper limb (354.4)
355.79
Other mononeuritis of lower limb
355.8 Mononeuritis of lower limb,
unspecified
355.9 Mononeuritis of unspecified site
Causalgia NOS
Excludes: causalgia:
lower limb (355.71)
upper limb (354.4)
356 Hereditary and idiopathic peripheral neuropathy
356.0 Hereditary peripheral neuropathy
Déjérine-Sottas disease
356.1 Peroneal muscular atrophy
Charcot-Marie-Tooth disease
Neuropathic muscular atrophy
356.2 Hereditary sensory neuropathy
356.3 Refsum's disease
Heredopathia atactica
polyneuritiformis
356.4 Idiopathic progressive
polyneuropathy
356.8 Other specified idiopathic
peripheral neuropathy
Supranuclear paralysis
356.9 Unspecified
357 Inflammatory and toxic neuropathy
357.0 Acute infective polyneuritis
Guillain-Barre syndrome
Postinfectious polyneuritis
357.1 Polyneuropathy in collagen
vascular disease
disseminated lupus erythematosus (710.0)
polyarteritis nodosa (446.0)
rheumatoid arthritis (714.0)
357.2 Polyneuropathy in diabetes
357.3 Polyneuropathy in malignant
disease
357.4 Polyneuropathy in other diseases
classified elsewhere
amyloidosis (277.3)
beriberi (265.0)
deficiency of B vitamins (266.0-266.9)
diphtheria (032.0-032.9)
hypoglycemia (251.2)
pellagra (265.2)
porphyria (277.1)
sarcoidosis (135)
uremia (585.9)
Excludes: polyneuropathy in:
herpes zoster (053.13)
mumps (072.72)
357.5 Alcoholic polyneuropathy
357.6 Polyneuropathy due to drugs
Use additional E code to
identify drug
357.7 Polyneuropathy due to other toxic
agents
Use additional E code to
identify toxic agent
357.8 Other
357.81
Chronic inflammatory demyelinating polyneuritis
357.82
Critical illness polyneuropathy
Acute motor neuropathy
357.89
Other inflammatory and toxic neuropathy
357.9 Unspecified
358 Myoneural disorders
358.0 Myasthenia gravis
358.00 Myasthenia gravis without
(acute) exacerbation
358.01 Myasthenia gravis with
(acute) exacerbation
Myasthenia gravis in crisis
358.1 Myasthenic syndromes in diseases
classified elsewhere
Amyotrophy from stated cause
classified elsewhere
Eaton-Lambert syndrome from
stated cause classified elsewhere
botulism (005.1)
diabetes mellitus (250.6)
hypothyroidism (244.0-244.9)
malignant neoplasm (140.0-208.9)
pernicious anemia (281.0)
thyrotoxicosis (242.0-242.9)
358.2 Toxic myoneural disorders
Use additional E code to
identify toxic agent
358.8 Other specified myoneural
disorders
358.9 Myoneural disorders, unspecified
359 Muscular dystrophies and other myopathies
Excludes: idiopathic polymyositis (710.4)
359.0 Congenital hereditary muscular
dystrophy
Benign congenital myopathy
Central core disease
Centronuclear myopathy
Myotubular myopathy
Nemaline body disease
Excludes: arthrogryposis multiplex
congenita (754.89)
359.1 Hereditary progressive muscular
dystrophy
Muscular dystrophy:
NOS
distal
Duchenne
Erb's
fascioscapulohumeral
Gower's
Landouzy-Déjérine
limb-girdle
ocular
oculopharyngeal
359.2 Myotonic disorders
Dystrophia myotonica
Eulenburg's disease
Myotonia congenita
Paramyotonia congenita
Steinert's disease
Thomsen's disease
359.3 Familial periodic paralysis
Hypokalemic familial periodic
paralysis
359.4 Toxic myopathy
Use additional E code to
identify toxic agent
359.5 Myopathy in endocrine diseases
classified elsewhere
Addison's disease (255.4)
Cushing's syndrome (255.0)
hypopituitarism (253.2)
myxedema (244.0-244.9)
thyrotoxicosis (242.0-242.9)
359.6 Symptomatic inflammatory myopathy
in diseases classified elsewhere
amyloidosis (277.3)
disseminated lupus erythematosus (710.0)
malignant neoplasm (140.0-208.9)
polyarteritis nodosa (446.0)
rheumatoid arthritis (714.0)
sarcoidosis (135)
scleroderma (710.1)
Sjögren's disease (710.2)
359.8 Other myopathies
359.81
Critical illness myopathy
Acute necrotizing myopathy
Acute quadriplegic myopathy
Intensive care (ICU) myopathy
Myopathy of critical illness
359.89
Other myopathies
359.9 Myopathy, unspecified
DISORDERS OF THE EYE AND ADNEXA (360-379)
360 Disorders of the globe
Includes: disorders affecting
multiple structures of eye
360.0 Purulent endophthalmitis
360.00
Purulent endophthalmitis, unspecified
360.01
Acute endophthalmitis
360.02
Panophthalmitis
360.03
Chronic endophthalmitis
360.04
Vitreous abscess
360.1 Other endophthalmitis
360.11
Sympathetic uveitis
360.12
Panuveitis
360.13
Parasitic endophthalmitis NOS
360.14
Ophthalmia nodosa
360.19
Other
Phacoanaphylactic endophthalmitis
360.2 Degenerative disorders of globe
360.20
Degenerative disorder of globe, unspecified
360.21 Progressive high
(degenerative) myopia
Malignant myopia
360.23
Siderosis
360.24
Other metallosis
Chalcosis
360.29
Other
Excludes: xerophthalmia (264.7)
360.3 Hypotony of eye
360.30
Hypotony, unspecified
360.31
Primary hypotony
360.32
Ocular fistula causing hypotony
360.33
Hypotony associated with other ocular disorders
360.34
Flat anterior chamber
360.4 Degenerated conditions of globe
360.40
Degenerated globe or eye, unspecified